Uso de lipasa acida lisosomal humana (lal) para preparar medicamento util para mejorar la funcion hepatica en un paciente humano.

摘要

The present invention provides methods of treating LAL deficiency comprising administering to a mammal a therapeutically effective amount of lysosomal acid lipase with an effective dosage frequency. Methods of improving growth and liver function, increasing LAL tissue concentration, and increasing LAL activity in a human patient suffering from LAL deficiency are also provided.