PHENYLALANINFREIES DIAETETIKUM FUER JUVENILE UND ADULTE PERSONEN MIT PHENYLKETONURIE

摘要

A phenylalanine-free diet based on amino acids for juveniles and adults having phenylketonuria which contains up to at least 95% of amino acids and preferably exclusively the following amino acids L-histidine, L-isoleucine, L-valine, L-threonine, L-methionine, L-leucine, L-tryptophan, L-tyrosine and L-lysine. In the process for the preparation of a phenylalanine-free diet, the amino acids employed and the other components which may be present are together dissolved or dispersed in water and then spray-dried. The powder obtained in this way does not demix and is readily pourable.